Many congenital anomalies of the lung in childhood have been described. Included is Congenital Cystic Adenomatoid
Malformation also known as Congenital lobar Adenomatosis, Adenomatoid Hamartoma, Pulmonary Adenoma, and
Congenital Bronchiolar Malformation in some literature.5 There are nine cases of CCAM diagnosed at the Philippine
Heart Center since its establishment. Two of these are rare in as much as they also had associated cardiac anomalies.
The first case has an associated Total Anomalous Pulmonary Venous Connection to the Superior Vena Cava and Atrial
Septal Defect secundum type while the second case has Atrial Septal Defect, primum type. Both patients underwent
lobectomy. The first case also underwent correction of the cardiac anomaly. Both patients were discharged improved.
The objective of this paper is to present and describe two unique cases of CCAM with coexisting congenital heart disease in children admitted at the Philippine Heart Center.